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Post by neurology admin on Jun 27, 2012 1:31:12 GMT -5
Diencephalic syndrome is a rare cause of failure to thrive in infancy and early childhood. The syndrome is characterized by profound emaciation with normal caloric intake, absence of cutaneous adipose tissue, locomotor hyperactivity, euphoria, and alertness (1). It commonly occurs in association with chiasmatic and hypothalamic gliomas (1¨C6). It has also been described in association with other lesions, such as midline cerebellar astrocytoma, suprasellar ependymoma, suprasellar spongioblastoma, and thalamic tumor (pathologic specimens not obtained) (7¨C11). We retrospectively reviewed the clinical and imaging findings in a series of children with diencephalic syndrome due to hypothalamic/chiasmatic astrocytomas. www.ajnr.org/content/18/8/1499.full.pdf
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